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Keywords: Motoneuron
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Journal Articles

Vascular regression precedes motor neuron loss in the FUS (1-359) ALS mouse model

In collection:
Neurodegeneration
Martin Crivello, Marion C. Hogg, Elisabeth Jirström, Luise Halang, Ina Woods, Megan Rayner, Karen S. Coughlan, Sebastian A. Lewandowski, Jochen H. M. Prehn
Journal: Disease Models & Mechanisms
Dis Model Mech (2019) 12 (8): dmm040238.
https://doi.org/10.1242/dmm.040238
Published: 13 August 2019
....2013.10.009 Kieran , D. , Sebastia , J. , Greenway , M. J. , King , M. A. , Connaughton , D. , Concannon , C. G. , Fenner , B. , Hardiman , O. and Prehn , J. H. M. ( 2008 ). Control of motoneuron survival by angiogenin . J. Neurosci.   28 , 14056 - 14061...
View article titled, Vascular regression precedes motor neuron loss in the FUS (1-359) ALS mouse model
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Includes: Supplementary data
Journal Articles

Loss of Ranbp2 in motoneurons causes disruption of nucleocytoplasmic and chemokine signaling, proteostasis of hnRNPH3 and Mmp28, and development of amyotrophic lateral sclerosis-like syndromes

In collection:
Neurodegeneration
Kyoung-in Cho, Dosuk Yoon, Sunny Qiu, Zachary Danziger, Warren M. Grill, William C. Wetsel, Paulo A. Ferreira
Journal: Disease Models & Mechanisms
Dis Model Mech (2017) 10 (5): 559–579.
https://doi.org/10.1242/dmm.027730
Published: 1 May 2017
... nucleocytoplasmic transport, ribostasis and proteostasis; however, cause-effect mechanisms of Ran GTPase modulators in motoneuron pathobiology have remained elusive. The cytosolic and peripheral nucleoporin Ranbp2 is a crucial regulator of the Ran GTPase cycle and of the proteostasis of neurological disease-prone...
View article titled, Loss of Ranbp2 in <span class="search-highlight">motoneurons</span> causes disruption of nucleocytoplasmic and chemokine signaling, proteostasis of hnRNPH3 and Mmp28, and development of amyotrophic lateral sclerosis-like syndromes
Open the PDF for Loss of Ranbp2 in <span class="search-highlight">motoneurons</span> causes disruption of nucleocytoplasmic and chemokine signaling, proteostasis of hnRNPH3 and Mmp28, and development of amyotrophic lateral sclerosis-like syndromes in another window
Includes: Supplementary data
Journal Articles

Loss of the Coffin-Lowry syndrome-associated gene RSK2 alters ERK activity, synaptic function and axonal transport in Drosophila motoneurons

Katherina Beck, Nadine Ehmann, Till F. M. Andlauer, Dmitrij Ljaschenko, Katrin Strecker, Matthias Fischer, Robert J. Kittel, Thomas Raabe
Journal: Disease Models & Mechanisms
Dis Model Mech (2015) 8 (11): 1389–1400.
https://doi.org/10.1242/dmm.021246
Published: 1 November 2015
... of the pathophysiological consequences. Using the fly neuromuscular system as a model for excitatory glutamatergic synapses, we show that removal of RSK function causes distinct defects in motoneurons and at the neuromuscular junction. Based on histochemical and electrophysiological analyses, we conclude that RSK...
View article titled, Loss of the Coffin-Lowry syndrome-associated gene RSK2 alters ERK activity, synaptic function and axonal transport in Drosophila <span class="search-highlight">motoneurons</span>
Open the PDF for Loss of the Coffin-Lowry syndrome-associated gene RSK2 alters ERK activity, synaptic function and axonal transport in Drosophila <span class="search-highlight">motoneurons</span> in another window
Includes: Supplementary data