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Keywords: Limb-girdle muscular dystrophy type 2A
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Journal Articles
Biol Open (2020) 9 (9): bio048975.
Published: 4 September 2020
... probes to detect activated-CAPN3 in cultured skeletal muscle cells. Calpain Calpain-3 Skeletal muscle Calpainopathy Limb-girdle muscular dystrophy type 2A Proteolysis Calpain (CAPN) is an intracellular non-lysosomal Ca 2+ -requiring cysteine protease (EC 3.4.22.17; Clan CA, family C02...